Abstract

INTRODUCTION:PERSISTENT HYPERPLASTIC PRIMARY VITREOUS IS A COMMON CONGENITAL DEVELOPMENTAL ANOMALY OF THE EYE THAT RESULTS DUE TO FAILURE OF THE EMBRYOLOGICAL, PRIMARY VITREOUS AND HYALOID VASCULATURE TO REGRESS.
PATIENT DETAILS :A 6 Y/F PRESENTED WITH BLINDNESS IN RIGHT EYE SINCE BIRTH.O/E: BCVA WAS OD:PL-NEGATIVE,OS: 20/20 .OD-MICROPHTHALMIA WAS PRESENT, CONJUNCTIVA AND CORNEA NORMAL,ANTERIOR CHAMBER WAS FUNNEL SHAPED, IRIS DIAPHRAGM HAD NO PUPILLARY APERTURE. OS- ANTERIOR AND POSTERIOR SEGMENT WERE NORMAL. SYSTEMIC EXAMINATION NORMAL. BSCAN OD-REVEALED SHORT AXIAL LENGTH. CONCAVE ECHOGENIC FOCI NOTED IN POSTERIOR TO POSTERIOR CAPSULE OF LENS IN VITREOUS CAVITY WITH ECHOGENIC MEMBRANE ATTACHED TO IT.
MRI ORBIT: REDUCED SIZE OF THE RIGHT OCULAR GLOBE. HYPERINTENSE THICKENED RETINAL LAYER NOTED IN THE DISTORTED RIGHT ORBIT WITH LINEAR STRUCTURE EXTENDING FROM THE OPTIC DISC TOWARDS THE POSTERIOR ASPECT OF THE LENS SUGGESTIVE OF PHPV.
CONCLUSION: PHPV CAN PRESENT WITHOUT LEUKOCORIA