Abstract

Sturge-Weber syndrome (SWS) is a phakomatosis involving the eyelids, conjunctiva, choroid, and retina. The mechanism of glaucoma in SWS involves developmental anomaly of anterior chamber angle and elevated episcleral venous pressure. Here, we present a case of Roach’s type II SWS with bilateral angle closure glaucoma (ACG) in a young adult, which, to the best of our knowledge, is the first-of-its-kind report in the literature. Though unusual, ACG may occur in young adults. However, the underlying causes that make them develop ACG are poorly understood. ACG is a rare presentation in SWS, which is usually a secondary angle closure mechanism. In the present case, the patient had ACG in the contralateral eye, too, and all possibilities of a secondary angle closure mechanism were ruled out with the help of investigations. We also highlight the importance of comprehensive clinical examination and appropriate investigations for early detection and proper treatment of such young ACG patients.