Abstract

Anterior segment dysgenesis (ASD) is defined as failed development of the anterior segment of ocular tissues, this includes a wide spectrum of conditions involving the cornea, iris, anterior chamber angle, and lens.
The authors experienced a rare case of secondary glaucoma combined with mesodermal dysgenesis of anterior segment, which disclosed extensive iridocorneal adhesion of congenital origin identical in both eyes in a 7-year-old boy. This kind of presentation is entirely different from the previously reported Axenfeld's and Rieger's anomalies as well as Peter’s anomaly. Highlights of this case- Sporadic presentation, bilateral extensive iridocorneal adhesions, cataractous lens, extensive posterior vitreous membranous hyperechoic shadows on ultrasound and no systemic associations. We report this interesting case with brief review of the literatures.