Abstract

A case report of 7 yr old boy from bikaner came to our opd with chief complaint of abnormal head posture, dancing eye movments and diminision of vision with his parents.
Purpose- to decribe the clinical characteristic of RIO palsy which is associated with other ocular anomaly.
Methods- clinical data is obtain from the patient chart- visual acuity, ocular alignment, ocular motility, cyclotortion, sterioacuity, parks 3 step test, slit lamp examination, indirect ophthalmoscopy, NCT& MRI.
Results- left hypertropia in primary position that increases in left gaze and with left head tilt.horizontal jerky nystagmus increse in direction of RIO muscle action and remain same in other direction. along with these finding RE partial aniridia, with LE iris atrophy with LE posterior polar cataract. neavus of ota present in both eye.
Conclusion- isolated IOP represent a rare condition in this case it cause is congenital basis without other significant neurological sign and symptoms.