Abstract
Introduction: Duane retraction syndrome is a congenital form of strabismus which is characterized by horizontal eye movement limitation and globe retraction with palpebral fissure narrowing during an attempted adduction. Method: A 6years old female child brought to the opd with complains of upwards and inwards rolling of left eye since birth. The parents noticed decrease in the size of the left eye and an increased tendency to move independently while looking to her sides. Her developmental age corresponded to around 6years. She had limited abduction movements in her left eye along with globe retraction and narrowing of the palpebral fissure while adduction was attempted. On external examination she had both large pinna. Her hemogram, renal function tests and thyroid profile were normal. Conclusion: Most cases of DRS are observed as isolated. The only known risk factor of an unilateral Duane syndrome is an affected parent, which leads to a 50% chance of passing the gene onto offspring.