Abstract

Purpose:To describe clinical characteristics and treatment outcomes of patients diagnosed with diffuse choroidal hemangiomas (DCH) in Sturge Weber syndrome
Methods: Retrospective study
Results:29 patients(32 eyes)were studied. Mean age at presentation was 21 months(0.1-57), unilateral in 26 patients(90%). Partial and total exudative retinal detachment(RD) were seen in 14 and 3 eyes, respectively. Pre-treatment mean tumor thickness was 5.05mm. Treatments administered were oral propranolol(n=4), external beam radiotherapy(n=3), plaque brachytherapy(n=9), transpupillary thermotherapy(n=3), and defer treatment(n=9). At mean follow-up of 94 months, complete(n=12)and partial regression(n=7) were noted with a mean reduction of tumor thickness to 2.85 mm and no significant change in mean BCVA(p< 0.05).
Conclusion:DCH in SWS is a rare intraocular tumor. Despite good tumor control with successful control of associated exudative RD with radiation treatment, visual acuity remained poor in 40.6 %.