Abstract

Benign familial fleck retina (BFFR) is characterized by postequatorial multifocal yellowish infiltrates at level of retinal pigment epithelium (RPE). Torpedo maculopathy is a rare, congenital, nonprogressive, oval-shaped, hypopigmented lesion, usually located temporal to the macula. This report describes a young male patient with bilateral macular sparing multiple yellow white retinal flecks situated beneath the retinal vessels. In the right eye, a torpedo-shaped hypopigmented lesion with a hyperpigmented temporal edge was observed temporal to the macula. There was mild thickening of retinal pigment epithelium on spectral-domain optical coherence tomography and retinal thinning and atrophy. Fundus autofluorescence showed multiple hyperfluorescent lesions around the posterior pole with a normal signal and a torpedo lesion of variegated autofluorescence in the right eye. The unusual coexistence of unilateral torpedo maculopathy with bilateral retinal flecks is being reported here.