Abstract

Study design:
Case report
Purpose:
Primary osteosarcoma of the orbit is a rare tumor. This report highlights its salient features and challenges in management.
Methods:
A 40 year old woman presented with progressive abaxial proptosis of left eye over two months with ocular motility restriction. Imaging revealed a mass lesion at the lateral aspect of left orbit with destruction of orbital wall. A left anterior orbitotomy with excision of mass was performed and the specimen sent for histopathological evaluation.
Results:
Histopathologically, the specimen revealed high vascularity with evidence of bone destruction and formation. Immunostains were positive for Smooth Muscle Actin, Desmin, CD-34. In absence of any systemic manifestations, a diagnosis of Primary Osteosarcoma was made.
Conclusion:
Primary osteosarcoma of the orbit is a rare tumour and diagnosis is based on histological features. Clear margins are challenging to obtain since frozen section of the bone cannot be done.