Abstract

Microspherophakia refers to a spherophakic lens with a decreased equatorial diameter. It can be found in systemic or ocular conditions, such as Marfan’s syndrome, Weill–Marchesani syndrome, iridocorneal endothelial syndrome, and Axenfeld–Rieger syndrome. It can be associated with complications secondary to the biconvex lens shape resulting in high myopia. Further, the zonular weakness of lens is prone to subluxation or even complete anterior or posterior dislocation. The anterior subluxation can lead to corneo-lenticular touch causing endothelial cell loss or endothelial decompensation.The authors describe a case of microspherophakia in a 8 years old girl detected incidentally.The child had presented with the history of loss of vision and pain in the left eye, allegedly after sustaining some sort of trauma while playing. She had diffuse corneal edema with rest details obscured.The IOP was elevated. The right eye examination after dilatation revealed the presence of microspherophakia.